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Enfanos 总部位于华盛顿州西雅图,专门开发酶和代谢物测定的试剂和方法。Enfanos 由华盛顿大学 Gelb 教授实验室的科学家于 2018 年创立,当时名为 GelbChem。20多年来,Gelb教授的实验室一直是新生儿筛查和先天性代谢缺陷诊断新技术开发的主导力量。Enfanos 正在为全球研究人员提供这些方法。


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Brand

SKUPruduct NameQuantity
ENFANOSBM40A-3  d5-C16:0 Sulfatide 3nmol
ENFANOSBM40D-3  d13-C16:1-OH-Sulfatide3nmol
ENFANOSQCEA-4Biomarker Qc DBs set, 3 Levels1 QC Set of 5 Spots per Level



产品列表:

Enzyme Assay Kits



1. Duplex Assay Kit for β-Hexosaminidase A and Total β-Hexosaminidase

2. plex Assay Kit for IDUA, GAA,GLA, GALC, GBA and ASMEnzymes

3. Galactosylceramidase Assay Kit

4. α-L-lduronidase Assay Kit

5. Acetylglucosamine-6-sulfataseAssay Kit

6. Heparan-a-glucosaminide N-acetyltransferase Assay Kit

7. Galactose-1-phosphateuridylyltransferase Assay Kit

8. Biotinidase Assay Kit

9. Duplex Assay Kit for Galactose-1-phosphate uridylyltransferase& Biotinidase

10. Lysosomal Acid Lipase Assay Kit

11. Palmitoyl Protein Thioesterase 1 Assay Kit

12. Tripeptidyl Peptidase 1 Assay Kit

13. Duplex Assay Kit for Palmitoy!Protein Thioesterase1&Tripeptidyl Peptidase1

14. Acid a-Glucosidase Assay Kit

15. α-Galactosidase A Assay Kit

16. Acid Sphingomyelinase Assay Kit

17. a-Mannosidase Assay Kit

18. a-L-Fucosidase Assay Kit

19. Sulfamidase Assay Kit

20. Arylsulfatase A Assay Kit

21. β-Galactosidase Assay Kit


Quality Control DBS



1. MegaQC DBs 3 Level Set(Enzyme Activity + Biomarker)

2. MegaQC DBs 9 Level Set(Enzyme Activity + Biomarker)

3. ARSA QC DBS Set, 3 Levels

4. Biomarker QC DBS Set, 3 Levels

5. Biomarker QC DBS Set, 7 Levels

6. Enzyme Activity QC DBs Set, 7 Levels

7. Enzyme Activity QC DBS Set,3 Levels

8. Psychosine DBS Calibrator Set

9. Endogenous GAG NRE Biomarker "UA-HNAc(1S)-Early" QC DBS

10. Endogenous GAG NRE Biomarker "UA-HNAc(1S)-Late" QC DBS

11. Endogenous GAG NRE Biomarker Kit (IDUA & 12S Deficiencies)

12. Endogenous GAG NRE Biomarker Kit (IDUA Deficiency)


Biomarker

d4-TCDCA

TCDCA

13C6-GIcNS-GIcUA(GAG Endogenous NRE)

GIcNS-GIcUA(GAG Endogenous NRE)

d6-GlcA-tetrol

GIcA-tetrol

d4-C26:0 LysoPC

C26:0 LysoPC 

d13-C16:1-0H-Sulfatide

Internal Standard for Endogenous GAG NRE Biomarkers

d5-LysoSM-509

LysoSM-509

d5-C16:0 Sulfatide

LysoGb3 (13C6-labeled)